A rare pathology in cardiological practice is idiopathic pulmonary arterial hypertension in a 3–year-old child.
https://doi.org/10.24412/2311-5068-2024-12-1-67
Abstract
Idiopathic (primary) arterial pulmonary hypertension in children is a very serious and urgent problem worldwide. The disease is extremely rare and has a serious prognosis for life due to the threat of sudden cardiac death. A case of diagnosis of the disease in a 3-year-old girl who began receiving therapy with a non-selective endothelin receptor antagonist and requires further careful monitoring is presented.
About the Authors
A. V. Lir
SAHCI AR Amur Regional Children’s Clinical Hospital
Russian Federation
Russian Federation
K. E. Naas
SAHCI AR Amur Regional Children’s Clinical Hospital
Russian Federation
Russian Federation
V. V. Shamraeva
Amur State Medical Academy of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
A. V. Tretyakova
Amur State Medical Academy of the Ministry of Health of the Russian Federation
Russian Federation
Russian Federation
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Review
For citations:
Lir A.V., Naas K.E., Shamraeva V.V., Tretyakova A.V. A rare pathology in cardiological practice is idiopathic pulmonary arterial hypertension in a 3–year-old child. Amur Medical Journal. 2024;12(1):68-74. (In Russ.) https://doi.org/10.24412/2311-5068-2024-12-1-67
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